Scienti c Publications on Portal Vein rombosis and Budd- Chiari Syndrome: a Global Survey of the Literature
نویسندگان
چکیده
Background & Aims: Portal vein thrombosis (PVT) and Budd-Chiari syndrome (BCS) are two rare vascular disorders of the liver that can lead to life-threatening complications. We conducted a global survey to systematically analyze the scienti c publications in the elds of PVT and BCS. Methods: All papers regarding PVT and BCS were identi ed via the PubMed, EMBASE, and Cochrane library databases. e publication year, country, type of paper, study design, and number of citations were summarized. Good quality papers were de ned as those in which a high proportion of homogeneous patients with BCS and/or PVT was observed. Results: We identi ed 6691 and 4325 papers regarding PVT and BCS, respectively. e number of papers gradually increased over time. Researchers from the USA published the greatest number of papers (PVT: n=1418; BCS: n=888). Clinical studies were the most common type of paper (PVT: n=5395; BCS n=3171), but fewer than half of these observed more than 10 patients (PVT: n=2667/5395; BCS: n=1092/3171). Furthermore, fewer than half of the clinical studies with more than 10 patients were of good quality (PVT: 976/2667; BCS: 466/1092). According to the study design, the good quality papers were classi ed as cohort studies (PVT: n=865; BCS: n=421), case-control studies (PVT: n=98; BCS: n=45), and randomized controlled trials (PVT: n=13; BCS: n=0). e 5 most frequently cited original articles and guidelines/consensuses were also listed. Conclusions: Despite an increase in the number of papers regarding PVT and BCS over time, most of the papers had a small sample size, suggesting the necessity of large cohort studies or randomized controlled trials.
منابع مشابه
A Rare Case of Budd Chiari Syndrome in a Child
A 7-year- old male child presented with the complaints of tense abdominal distension and swelling over feet since 1 month. The patient had repeated episodes of similar complaints since last two years with partial or complete relief after taking various forms of allopathic therapy. On imaging, Budd-Chiari syndrome was diagnosed which was hallmarked by occluded Inferior venacava (IVC), caudate lo...
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